Goodpasture a syndrome: Amachititsa, Zizindikiro ndi Njira Chithandizo

Goodpasture ndi matenda - ndi chosowa autoimmune matenda limodzi ndi m'badwo wa chitetezo atypical kuti aukire maselo a m'mapapo ndi impso. matenda ofanana ambiri amagwira amuna a zaka zapakati pa zaka 12 ndi 35 zakubadwa. Akukhulupirira kuti odwala ndi propensity majini ndi chisokonezo chotero.

syndrome Goodpasture akuti: zimayambitsa matenda

Kumene, wodwalayo anthu ali ndi kutengera za kumtundu matenda. Komabe, pali zinthu zimene zimachititsa kuti anachita autoimmune.

Ndi chitukuko cha matenda chitetezo cha m'thupi umabala chitetezo kuti kuukira Kakhungu woyambira wa capillaries wa alveoli m'mapapo mwanga ndi tubules aimpso. Chifukwa cha ndondomekoyi zimakhudzira ndi zimaphulika capillaries, kuchititsa magazi mkati ndi zizindikiro kugwirizana.

Kwa nthawi yoyamba matenda amenewa inalembedwa mu 1919. Koma lero si kudziwa zimene akapsa yankho m'thupi. Akukhulupirira kuti syndrome Goodpasture limayendera ndi matenda opatsirana. Nthawi zina kutsegula matenda chifukwa cha mankhwala ena ndi ziphe. Izo zalembedwa milandu zingapo zimene matendawa chinayamba pambuyo kumwa mankhwala.

syndrome Goodpasture akuti: zizindikiro

Childs, zizindikiro loyamba dongosolo kupuma. Wodwala anadandaula ululu pachifuwa, kawirikawiri chifuwa ndi kupuma movutikira pa yaikulu. Malinga hemoptysis imayamba ndi chitukuko cha matenda. Mapapo akhoza kumva yonyowa kapena youma wheezing. Wodwala akhoza kuona kutopa nthawi zonse ndipo kusinza. Nthawi zina pali kwambiri kuwonda chifukwa cha kuchepa minofu misa. Mosiyana ndi zimene ambiri amakhulupirira, capillaries m'maso si anakhudzidwa ndi matenda.

Popeza pali chachikulu yaing'ono kukha mwazi wa chizindikiro lotsatira - ndi kuchepa magazi kapena kuchepa kwa magazi m'thupi. Ngati inu kufufuza mtima, izo Tingaone kuti khungu lake kwambiri wotumbululuka. Pali cyanosis wa nembanemba wa mucous. Nthawi zina, kutupa nkhope kuonekera. Kutentha ambiri kuchuluka.

Zizindikiro za matenda mu impso kuoneka pang'ono kenako. Mungaone kusankha pang'ono magazi mu mkodzo. Aimpso kulephera amakula mwamsanga ndipo limodzi ndi zizindikiro zake.

syndrome Goodpasture akuti: njira yodziwira

Pofuna kuti matenda, dokotala ayenera bwinobwino mtima kuona zotsatira ndi mayesero ECG. Ambiri, kusanthula magazi Tingaone chitsulo akusowa magazi m'thupi ndi kuchuluka leukocyte chizengerezo; kuchuluka ESR. Urinalysis detects mkodzo zambiri zomanga thupi ndi maselo ofiira. Muyenera ndithudi kufufuza sputum, monganso anapeza maselo ofiira. Akhala akugwira ndi spirography kumathandiza kudziwa kuyan'anila za kupuma kunja. Perekani komanso ECG kuphunzira mpweya magazi, x-ray ndi biopsy a minofu kuonongeka, zomwe zimathandiza kuti kuika matenda okhazikika.

syndrome Goodpasture akuti: Abereke

Ndipotu, madokotala ananena zawo kwa odwala ngati ndi zovuta. Ndipo chinthu chofunika kwambiri apa - nthawi ndi matenda ndi kuyamba chithandizo msanga.

Mwatsoka, mankhwala enieni matenda amenewa alipo. Koma ananena kuti nthawi zambiri, okwanira mankhwala syndrome ntchito umatsika mkati miyezi 6-9. Ngati inu chingaimitse chitukuko cha matenda aimpso ndi m'mapapo mwanga, wodwalayo kupulumuka. Childs, madokotala mankhwala angapo kulandira corticosteroids. Plasmapheresis imagwiridwa, ngati n'koyenera - magazi , ndipo ngakhale impso kupatsidwa zina. Pofuna kuletsa kukula kwa magazi m'thupi ndi akusowa chitsulo kukhuta mankhwala oyenera. Koma nthawi zina, mu Zikavuta kwambiri, magazi ali wofunikila Kupha magazi m'thupi.