Thanzi, Matenda ndi zokwaniritsa
Matenda demyelinating polyneuropathy: maonekedwe, mitundu, zimayambitsa, zizindikiro ndi mankhwala
Demyelinating polyneuropathy - matenda aakulu amene anatsagana ndi kutukusira kwa muzu mitsempha ndi kuonongeka mwapang'onopang'ono ndi myelin m'chimake. Ndi khalidwe labwino yake ya mankhwala a matenda angathe kuthetsedwa kupewa mavuto aakulu. Choncho n'kofunika kudziwa waukulu zimayambitsa ndi zizindikiro za matenda, nthawi kuwona dotolo.
matenda ndi chiyani? mwachidule
Mwakucimbidza Dziwani kuti matenda ali osowa - 100 zikwi anthu 1-2 kokha amadwala ndi matenda ofanana. Kodi sitichedwa matenda amuna achikulire, ngakhale akazi ndi ana akhoza anakumana ndi matenda amenewa. Monga ulamuliro, demyelinating polyneuropathy limodzi ndi chotupa symmetrical a mizu mitsempha, chifukwa mu kufooka kukula kwa wapotalikira ndi proximal m'makona minofu. Mwa njira, nthawi zambiri, matenda amagwirizana ndi matenda Guillain-Barré. Ndipo lero ndi osadziwika ngati aakulu yotupa demyelinating polyneuropathy, matenda osiyana kapena mawonekedwe zizindikiro zatchulidwazi.
The chikuchititsa mavuto a matenda
Mwatsoka, zimayambitsa ndi njira ya chitukuko cha matendawa kwa tsiku samadziwidwa mpaka kumapeto. Komabe, maphunziro yaitali asonyeza kuti yotupa demyelinating polyneuropathy - matenda autoimmune. Pazifukwa zosiyanasiyana, chitetezo cha m'thupi ayamba kulandira thupi maselo yekha kunja, chifukwa zipatso oteteza yeniyeni. Pankhaniyi, antigens izi kuukira mitsempha muzu minofu, kuchititsa chiwonongeko cha myelin m'chimake, kuchititsa kutupa. Choncho, misempha kutaya katundu pamoyo, imbaenda kusokoneza innervation minofu ndi zina ziwalo.
Pankhaniyi, ndi chilichonse matenda pafupifupi ena autoimmune, pali majini. Komanso, pali zinthu zingapo zomwe angasinthe chitetezo cha m'thupi. Zikuphatikizapo kagayidwe kachakudya ndi mahomoni disruptions, kwadzaoneni m'thupi ndi m'maganizo nkhawa, zoopsa, nkhawa, matenda aakulu, matenda a thupi, vaccinations, opaleshoni.
Demyelinating polyneuropathy: Gawo
Mu mankhwala amakono, pali masikimu angapo a gulu la matenda. Mwachitsanzo, malinga ndi vuto olekanitsidwa siligwirizana, zoopsa, yotupa, poizoni, ndi mitundu ina ya matenda. Malinga Pathomorphology amatha kusiyanitsa palokha demyelinating ndi axonal polyneuropathy zosiyanasiyana.
Tiyenera kulankhula za chikhalidwe cha matenda:
- Pachimake demyelinating polyneuropathy akufotokozera msanga - pa matenda kwenikweni ndi galimoto kukhala pa masiku angapo kapena masabata.
- Mu mawonekedwe subacute matenda si kukula mwamsanga, koma ndi msanga - kuchokera masabata angapo miyezi isanu ndi umodzi.
- Matenda polyneuropathy imatengedwa zoopsa kwambiri chifukwa amatha chobisika. Kukula kwa matendawa akhoza mzaka zingapo.
Zizindikiro zazikulu za matenda
Chithunzi matenda mu matenda kumatengera zifukwa zambiri, kuphatikizapo mtundu wa matenda, ndi chifukwa cha chitukuko, mtima makamaka ndi m'badwo wake. Demyelinating polyneuropathy, makamaka mu magawo oyambirira limodzi ndi minofu kufooka ndi ena chisokonezo imalandira. Mwachitsanzo, odwala zina amadandaula yafupika tilinazo mu miyendo, kuwotchedwa kutengeka ndi kumva kulasalasa. Pakuti mtundu pachimake cha matenda yodziwika ndi maonekedwe a zowawa amphamvu girdling. Koma pamene izo zifika ku chiwonongeko aakulu a mizu mitsempha, kupweteka sangakhale kwambiri kutchulidwa kapena kwina palimodzi.
Ndi paresthesias wa malekezero kuoneka ngati ndondomeko ili m'kati. Pa kuyenderako muona kuchepa kapena kusapezeka kwa bongo tendon kapena mofulumira wawo wonse. Nthawi zambiri izo dongosolo demyelination chimakwirira misempha ya miyendo, koma n'zotheka kugonja misempha ena. Mwachitsanzo, odwala ena amadandaula dzanzi lilime ndi malo kuzungulira pakamwa. Kwambiri kamodzikamodzi anaona kumwamba paresis. Mmenemonso, wodwalayo kovuta kumeza chakudya kapena malovu.
Axonal-demyelinating polyneuropathy: Mitundu ndi Zizindikiro
Chiwonongeko cha axons zambiri chifukwa cha zotsatira poizoni m'thupi. mawonekedwe Axonal matendawa lagawidwa mitundu yambiri yakuti:
- Pachimake polyneuropathy nthawi zambiri amayamba ndi chamoyo aakulu poizoni (mwachitsanzo, ndi okusayidi wa Arsenic ndi poizoni ena oopsa). Zizindikiro za matenda ya ubongo kuoneka mwachilungamo msanga - pambuyo masiku 14-21 wodwala Tingaone paresis wa miyendo m'munsi ndi chapamwamba.
- Subacute mawonekedwe a matenda mwina chifukwa cha poyizoni ndipo aakulu kagayidwe kachakudya wonongeka. Zizindikiro zazikulu angathe pa masabata angapo (nthawi zina miyezi 6).
- Matenda axonal neuropathy akufotokozera pang'onopang'ono, nthawi zina ndondomeko amatenga zaka zoposa zisanu. Kawirikawiri, izi mawonekedwe amagwirizana ndi kukhalapo kwa kutengera za kumtundu, komanso kuledzera yaitali chamoyo (pali Mwachitsanzo, chidakwa aakulu).
njira matenda
Only ndi dokotala wodziwa akhoza oterewa "demyelinating polyneuropathy." Matenda a matenda - ndondomeko zovuta, limene lili ndi mfundo zazikulu zochepa. Kuyamba, kupanga ndandanda Kupenda thupi ndi mndandanda wa mbiri yonse. Ngati wodwalayo sensorimotor neuropathy kuti akufotokozera zosachepera miyezi iwiri, ndiye chifukwa chabwino kwa matenda yolondola.
Kenako, monga ulamuliro, pansi atafufuza. Mwachitsanzo, miyezo ya mitsempha conduction mathamangidwe kwa zikhumbo pamodzi mitsempha galimoto angasonyeze kuchepetsa zowonetsera. Ndipo phunziro zasayansi wa madzimadzi kuchuluka misinkhu cerebrospinal mapuloteni anati.
Kodi mankhwala amapereka mankhwala amakono?
Amene mankhwala amafuna demyelinating polyneuropathy? Chithandizo mu nkhani iyi imakhala zinthu zingapo, kutanthauza kuchotsa kutupa, ndi yimitsira wa ntchito chitetezo cha m'thupi ndiponso thandizo.
Pa exacerbation kutupa ndi kukhalapo kwa odwala amphamvu Kwalamulidwa m'thupi odana ndi yotupa mankhwala, ndicho corticosteroids. Zothandiza kwambiri "Prednisolone" ndi analogues ake. Therapy imayamba ndi mlingo wa Kumwambamwamba, amene amachepetsa monga mofulumira zizindikiro. Childs, minofu mphamvu akuyamba kubwerera patapita masabata ochepa. Koma Dziwani kuti yaitali ntchito mankhwala akhoza kuyambitsa zotsatira zina zoyipa.
Odwala matenda aakulu Kawirikawiri analimbikitsa plasmapheresis, amene amapereka zotsatira zabwino ndiponso kukwaniritsa chikhululukiro. Komanso, odwala kutumikiridwa mankhwala akhoza ziletsa ntchito chitetezo cha m'thupi - iwo ayenera kutenga maphunziro pafupifupi moyo. Imodzi mwa njira yatsopano ya mankhwala amakono ndi mtsempha immunoglobulin.
Kuti madokotala ananena zawo odwala ndi polyneuropathy
Zotsatira mu nkhani iyi zimadalira mawonekedwe a matenda, khalidwe la mankhwala, komanso ena mwa makhalidwe munthu wa chamoyo. Mwachitsanzo, munthu ndi maonekedwe pachimake matenda, amene mwamsanga mankhwala zofunika, zotsatira za matenda mosavuta kwambiri. Ndipo ngakhale kuchira bwino chingapezeke n'komwe nthawi zonse, odwala ambiri kubwerera ku moyo wabwinobwino.
Koma aakulu demyelinating polyneuropathy, amene akufotokozera pang'onopang'ono pa zaka zingapo, kungachititse kuti kuwonongeka chosachiritsika wamanjenje dongosolo, kulumala ngakhale imfa. Mwa njira, nthendayo anasamutsa odwala okalamba kwambiri kwambiri.
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