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Yoopsa Mowa Syndrome. Mowa pa mimba

Madokotala sikuli chabe nthawi zonse anachenjeza za kuopsa mowa, makamaka pa mimba. Kuwonjezera pa kungasokoneze thupi la mayi, sukhala wa mwana wosabadwayo m'mimba - mwana amene alibe ngakhale sadabadwe.

oopsa mmene mowa pa mimba?

Wamphamvu mankhwala teratogen, Mowa kumabweretsa kuwonongeka zambiri mwana wosabadwayo. Iye mofulumira mitanda ya latuluka chotchinga afika kwa mwana, ndipo ndende zake mwazi wa mwana zambiri kuposa mayi. Mwana machitidwe enzyme nawo kagayidwe Mowa, sangamvetse n'chongoletsa mowa. Chifukwa, mpweya si amaperekedwa kwa mwana wosabadwayo, zomwe kwenikweni zimakhudza chitukuko ndi mapangidwe, kuchititsa maonekedwe a syndrome mowa yoopsa.

Amaganiza kuti mlingo yovuta Mowa kwa khanda m'mimba liri 30-60 ml ya patsiku. Komabe, akatswiri ambiri amakhulupirira kuti ndalama otetezeka mowa basi sizichitika.

zipatso akuwululidwa zotsatira embryotoxic Mowa pa mimba. Kumwa mowa pa trimester zimayambitsa pachiopsezo chachikulu chotenga vuto lobadwa ndi yoopsa imfa trimester chachiwiri - structural CNS matenda. Mu masiteji wotsiriza wa mimba, kudalira izi zingachititse yoopsa kukula retardation.

Kodi syndrome mowa yoopsa?

Izi ndi gulu la malformations kobadwa nako ana, chifukwa cha zotsatira teratogenic Mowa. kudwala Izi amakhala ndi akuchedwa chitukuko mwana lathupi ndi maganizo, dysmorphic mawonetseredwe ochuluka, retardation maganizo ndi olumala ena.

Yoopsa Mowa Syndrome - ndi chizindikiro, amene anapezeka ku ana amene amayi amadwala uchidakwa aakulu. Maziko a chiyambi cha matenda ndi kukhudzana ndi poizoni zoipa ethyl mowa ndi mankhwala ake kuwonongeka pa mwana wosabadwayo mkati m'mimba. Izi ndi zotheka ndi kudya kuwoloka latuluka Mowa izi zimakhudza chiwindi, RNA kaphatikizidwe ndi zoyendera wa kufufuza zinthu zambiri.

Pafupipafupi kubadwa kwa ana ndi kudwala izi zimasiyanasiyana anthu awiri mpaka asanu pa kubadwa 1000. M'mayiko ena, Chiwerengerochi ndi apamwamba kwambiri. Akatswiri mwazindikira chizolowezi amphamvu: kubadwa kwa mwana wake woyamba ndi makolo aakulu kakulidwe olumala sakuyandikira mfundo - mwana wachiwiri ndipo kenako mu 70% milandu zimachitika ndi matenda omwewo.

A mbiri pang'ono

wosabadwa woyamba mwa mimba uchidakwa wafotokozedwapo asayansi P. Lemoine. Iye anaphunzira gulu la ana a azimayi akuvutika ndi vuto, napeza matenda ena kakulidwe. Kenako, KL Jones ananena mu ntchito za kupatuka ana amene amayi awo sanali amakana kumwa mowa pa mimba. Mwa kaphatikizidwe maphunziro awiri, asayansi kuitana kuyan'anila awa "syndrome yoopsa mowa". Popeza madokotala padziko lonse ayamba mwakhama kufufuza kudwala.

Atafufuza mu CIS amasonyeza kuti kugonana chilungamo alibe mfundo zolondola za kuopsa mowa. N'chifukwa chake chokha ena amapatula iwo ali woyembekezera. akazi ambiri molakwa kuti vinyo wofiira ndi zoipa kwa mwana wosabadwayo osati ndipo ngakhale kumathandiza kuti mapangidwe ake olondola. Malinga ndi kafukufuku, pafupifupi 80% ya amayi kumwa mowa pamaso mimba, ndi 20% sasiya iwo mpaka pamene mwana wabadwa.

chithunzi matenda

syndrome yoopsa mowa - chifukwa chachikulu cha kulumala aluntha mwana. Iwo akhoza kutenga maonekedwe a matenda chapakati mantha dongosolo, matenda a khalidwe ndi nzeru. Nthawi zambiri ana ndi matenda lino zomwe zikutsalirazi kumbuyo kulemera ndi kutalika. Iwo amasiyana maonekedwe khalidwe: adzafupikitsidwa palpebral fissures, woonda chapamwamba mlomo, ndi poyambira labial zayamba si anasonyeza. Nthawi zina microcephaly ndi ptosis atumwi. Chotero anomalies nkhope Liunikeni moyo. kuvutika aakulu ndi matenda a mtima, dysplasia zimfundo ndi chifuwa chilema.

syndrome yoopsa mowa ana yodziwika ndi mkhutu kumva ndi masomphenya, ulesi. Iwo sakuzindikira ndipo kumbukirani mfundo sukulu, kudziletsa pang'ono pa maganizo awo. Ana ameneŵa kovuta kuti azolowere timu, sadziwa mmene kukhala abwenzi ndi anzawo, kotero kawirikawiri amalangiza maphunziro m'masukulu apadera yogonera komweko.

kudwala diagnostics

Neonatologist nthawi yomweyo pambuyo pa kubadwa kwa mwana ku matenda syndrome mowa yoopsa. Mbali khalidwe la kudwala imeneyi, zambiri kumaoneka kuti apoyera (otsika kutalika / kulemera, kuvutika kunja). M'pofunikanso kuganizira pamaso pa otchedwa mbiri zoledzeretsa mayi.

biomarkers achilendo protrude akufotokozera tsitsi ndi meconium mafuta asidi esters. thandizo yokulirapo kupereka matenda okhazikika njira neuroimaging. Zikuphatikizapo Kujambula a ubongo ndi neurosonography. Kuti achotse chisokonezo kwambiri za chitukuko cha ana kuchita ECG, ultrasound wa akugwirira.

Anasintha kuwunika mwanayo ndi matenda a "syndrome yoopsa mowa" ikuchitika ndi akatswiri.

Kodi chithandizo chofunika?

kudwala Izi si mankhwala. Komabe, panthawi yake mwina kwa akatswiri akhoza kwambiri tisaletse miyoyo ya achinyamata amene akudwala. Ena zizindikiro ndi amenable kukonza ndi opaleshoni (chisokonezo kwa mtima, m'mimba thirakiti). Kuthetsa zopindika maxillofacial akutsatiridwa opaleshoni pulasitiki.

Penyetsetsani ndi katswiriyu kumalimbikitsa kudzudzulidwa moperewera zolakwika ku CNS. ana onse ndi matenda uyu ayenera kuonedwa ndi zamaganizo a. katswiri angakuthandizeni mwanayo kuti azolowere anthu, makamaka asiye khalidwe lake.

Kuneneratu ndi kapewedwe

Ana ndi matenda kawirikawiri moyo wawo wonse mu mabungwe, ndipo pambuyo - mu chiphaso psycho-ubongo. Iwo ali makolo kosafunikira ndipo sangathe kusamalira yokha.

Pakuti kupewa matenda mowa yoopsa mu mwana wa akazi onse a msinkhu wobereka ayenera ayesedwa ndi chizindikiritso yake ya magulu otchedwa chiopsezo. Iwo akhoza kulowa madona amene amakonda kumwa mowa. Nthawi zambiri, akazi ambiri sakudziwa nkomwe mowa mmene oopsa pa mimba ya mwana wosabadwa. Madokotala ayenera kukhala ntchito zonse pa kuchepetsa kapena kutha kwathunthu mowa mkazi. Amene sangakwanitse paokha chizolowezi choipachi, muyenera kutumiza kwa chithandizo chapadera.

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