ThanziMatenda ndi zokwaniritsa

Tolosa-Hunt syndrome: matenda ndi mankhwala

Ngakhale mkulu mlingo wa chitukuko cha mankhwala, matenda ena omwe sanapite mpaka kumapeto. Kuti amodzi mwa matenda amenewa anafotokoza syndrome Tolosa-Hunt. Pakali pano pali zizindikiro chabe ya matenda, pamene zifukwa sanafikebe anafotokoza. Ambiri mwina, ichi ndi chifukwa chakuti matendawa ali osowa kwambiri ndi lotsegula osati kale. Komanso, syndrome Tolosa-Hunt zambiri "masked" ndi pathologies ena, ndipo n'zosavuta kusokoneza. The chizindikiro chachikulu ndi matenda diso ndi misempha cranial. Amadziwika kuti chimodzi mwa zizindikiro za matenda akuti ndi chakuti kuti labwino mankhwala timadzi, kenako mwamsanga bwino. Komabe, muyambirenso angayambe nthawi iliyonse.

Kufotokozera syndrome Tolosa-Hunt

Kutchula koyamba za matenda wawonekera ndi posachedwapa. Limafotokonzera 1961 ndi British maso Hunt. Kuwonjezera pa udindo waukulu, ndipo kudwala otchedwa mosiyana monga "chameleon". Ichi ndi chifukwa chakuti zizindikiro zake amafanana matenda ena ambiri. Pakati pawo: zotupa za mutu, matenda encephalitis, myositis mpita ndipo ngakhale matenda a dongosolo hematopoietic. Komanso, kudwala wa Tolosa-Hunt otchedwa chizindikiro cha kuposa yozungulira fissure kuti silikuimira molondola kusonyeza akamanena za vutolo. Chithunzi matenda a matenda kumatengera mtundu wa misempha ubongo anakhudzidwa. Nthawi zambiri, matenda Tolosa-Hunt amakhala ndi ululu mu zitsulo diso, kulephera kusuntha maso, diplopia. Pamene yake anayamba timadzi mankhwala akhoza kuchiza kapena chosunga chikhululukiro.

The aetiology wa syndrome Tolosa-Hunt

Chifukwa chakuti kudwala ali mawonetseredwe osiyana ndi amayamba mwadzidzidzi, si koma kuzindikira etiology enieni. Iwo unakambidwanso mogwirizana ndi zosayembekezereka otsika matendawa. Chifukwa cha zimenezi, madokotala simusowa bwinobwino tione matenda. Pali mfundo zingapo, chimene angayambe kudwala. Kuonetsetsa zifukwa zotsatirazi etiological akupezeka odwala matenda Tolosa-Hunt:

  1. Malformation. Mawu amenewa akusonyeza chitukuko nthenda ya dongosolo mtima wa diso. Chifukwa cha malformations ali osokonezeka venous ndi wolumikizira magazi, amene ayenera kukhala zachibadwa. kuphwanya Izi ndi ofala pakati pa akazi.
  2. Autoimmune mokwiya. Chinthu Ichi ndi choyambitsa cha matenda ambiri. Komabe, poyankha funso la chifukwa maselo mthupi anayamba kuwononga zimakhala za thupi, ndipo simungathe. Nthawi zambiri, "mokwiya" zikadzatha kuvutika maganizo, ndi nthawi ya njira panopa opatsirana.
  3. Osiyana ubongo zotupa ndi misempha cranial. Zimakhala monga zotupa chosaopsa ndi khansa.

Syndrome Development limagwirira

Popeza chakuti etiology matenda akhala wosadziwika, pathogenesis, nawonso zovuta kufufuza. Kaya zifukwa osauka kudwala amakhudza okha nyumba zina za maso ndi minofu mantha. Monga amadziwika, dzina lachiwiri la matenda - ndi matenda aakulu yozungulira fissure. Izi amagwirizana ndi pathogenesis, chifukwa kugonjetsedwa kwa mitsempha poyera ndi mitsempha kuti kudutsa izo. Choyamba pali kusintha kwa m'mitsempha ophthalmic ndi mtsempha wamagazi. Chifukwa cha kuvulala minofu trophism. Komanso, kuonongeka cavernous nkusani, umene uli pafupi ndi aakulu yozungulira fissure. Mtsempha wamagazi kupereka izo, kukhala chofuna ndi minofu hypertrophy. Monga mukudziwa, kudzera kusiyana kudzera zotsatirazi cranial misempha: chipika, kuchotsa mbali ya trigeminal ndi oculomotor. Nthawi zina, zinakhudza awiriawiri onsewa. Pa nthawi yomweyo amadwala luso atembenuza diso. Nthawi zina chakhungu ntchito ya awiriawiri imodzi kapena ziwiri misempha.

Tolosa-Hunt syndrome: zizindikiro

Kudwala kaŵirikaŵiri kumachititsa lokha anamva mu m'badwo pakati ndi akale. syndrome Izi zikhoza kukhala sachedwa akazi ndi amuna onse. Chithunzi matenda a matenda akufotokozera mwadzidzidzi popanda preconditions iliyonse. Kusiyanitsa zizindikiro zotsatirazi:

  1. Ululu m'munda ophthalmic. Kusapeza adzawonekera pa mphumi, zikope, mutu. Kenako nakweza mphamvu ya ululu, izo chimafikira kwa diso.
  2. Diplopia. Izi chizindikiro limapezeka pambuyo osauka ululu. Wodwala zikuwoneka kuti zinthu zonse zomwe zikuwoneka forked. Muziganizira kuyang'ana zovuta.
  3. Kuphwanya sayenda wa mwana wa m'diso la - ophthalmoplegia. Nthawi zambiri anaona ndi dzanja limodzi. mmene umadalira pa mphamvu ndi chiwerengero cha misempha anakhudzidwa.
  4. Kutupa conjunctiva lapansi.
  5. Exophthalmos. Inati, pakalibe chithandizo ndiponso musabise pafupipafupi.
  6. Strabismus. Kumachitika pamene mitsempha agwidwa mbali imodzi yokha.
  7. Low kalasi malungo ndi kuwonongeka.

zizindikiro zambiri kukula pang'onopang'ono ndi kutsatira mzake. Nthawi zina iwo anati imodzi. Zizindikiro za matenda mwadzidzidzi kutha, monga iwo anaonekera. Komabe, popanda chithandizo cha kudwala amasankha lokha anamva kachiwiri. Mlingo zisadzachitikenso konse zosiyana nthawi chikhululukiro.

Tolosa-Hunt syndrome: matenda kudwala

Kudziwa kudwala yovuta, monga zizindikiro zake zimafanana ndi matenda ena ambiri. Choncho Tolosa-Hunt syndrome imatengedwa ndi matenda a kupatulana. Wodwala woyamba kufunsidwa za maonekedwe a kupitilira matenda (kuyamba, monga zizindikiro kukhala). Pambuyo pake, mayesero zasayansi ndi diagnostics malangizo. Nkofunika kugwira ophthalmic ndi ubongo bwino. Kuti achotse ubongo zotupa, Kujambula imagwiridwa. M'pofunikanso kuchita ultrasound ndi X-ray Kupenda mwake diso. Pamaso pa malformations mtima anatsimikiza mtima angiography. Komanso, a muyezo wa matenda ndi mphamvu ya mankhwala timadzi. Ngati zasayansi ndi Kupenda malangizo anaulula palibe kusintha kutchulidwa, ndi zizindikiro mwamsanga kudzatha mankhwala, n'kutheka, matenda - Tolosa-Hunt syndrome. Prednisolone amagwiritsidwa ntchito pofuna kuchiza kwambiri.

Masiyanidwe matenda ndi matenda ena

The matenda poyerekeza ndi pathologies ena diso wamanjenje dongosolo. Sitepe yoyamba ndi kuti achotse njira yotupa ubongo ndi meninges ake, ndi zotupa. Ngati mukukayikira oumitsa khosi kapena encephalitis, ndi lumbar puncture imagwiridwa. Pofuna kupewa zotupa chosaopsa ndi odwala khansa anakumana Kujambula, ubongo CT mapanga sikani ndi X-ray a Chigaza lapansi. Matendawa kusiyanitsidwa lymphoma, cysts wa nkusani cavernous ndi thrombosis. Pamene zizindikiro zimenezi zingachitike ndi pathologies zokhudza zonse monga sarcoidosis, myositis kanjira, migraine, etc. Kuti apange matenda zolondola, wodwala ayenera kuona akatswiri osiyanasiyana: .. An maso, katswiriyu, mtima dokotala, ndi m'thupi yemwenso.

Chithandizo cha matenda Tolosa-Hunt

Chithandizo cha matenda Tolosa-Hunt ndi kuika mankhwala kubisa chitetezo cha m'thupi. Chifukwa chaichi, ndi timadzi munali mankhwala: "Prednisolone", "Hydrocortisone". Mankhwalawa ndi zotsatira mu pathologies ena autoimmune, koma zizindikiro matenda zikawoneka mwa masiku 3-4. syndrome, Tolosa-Hunt mankhwala ndi prednisolone ndi ku mawerengedwe a 1-2 mg / kulemera makilogalamu thupi. Ngati mankhwala ntchito mu mawonekedwe a njira, izo Kwalamulidwa kwa 500 1000 mg pa tsiku. Komanso, kugwiritsa ntchito mankhwala othetsa ululu ndi mavitamini.

Kuchita ndi vuto Tolosa-Hunt

Kawirikawiri, pamene matenda izi wolemala odwala opulumutsidwa. Muyenera kuonetsetsa kuti wodwala Tolosa-Hunt syndrome. Chilema mu kudwala uyu ali osowa. Komabe, pamene musabise pafupipafupi mwina tisonyezeni 3 gulu. Wodwala ayenera umasamutsidwa ku ntchito kuwala kuti sikutanthauza khama zithunzi. Komanso, pamene kulimbikira matenda mitsempha mtima sangasiye magalimoto ku kuphwanya kayendedwe diso ndi diplopia.

Syndrome Kuteteza Tolosa-Hunt

Pasadakhale kulosera za chitukuko cha matenda Tolosa-Hunt sizingatheke Choncho, kupewa chachikulu kulibe. Ngati pali zizindikiro monga ululu maso ndi pamphumi diplopia, muyenera kuchititsa matenda mokwanira. Pamene Tolosa-Hunt syndrome zofunika kuchita kupewa sekondale. Izi zikuphatikizapo yake timadzi mankhwala chitetezo chokwanira thandizo. Muyeneranso kupewa mavuto ndi njira yotupa.

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