Thanzi, Matenda ndi zokwaniritsa
Amniotic constriction: zimayambitsa, zizindikiro, matenda, ndi chithandizo kamwedwe
Nthawi zina amayi kukomoka wathanzi kubereka ana ndi zilema morphological: kupanda phalanges, miyendo ndi mitu. The mayi sangadziwe mlandu yekha kapena madokotala zomwe zinachitika kwa ana awo. Nthawi zina amabwera mlandu. Koma kodi chifukwa cha vuto lobadwa?
tanthauzo
Amniotic constriction, mwinamwake amatchedwa "amniotic msoko" kapena "chingwe Simonara" zikuimira dublication amnion nsalu zomwe lidakali pakati pa makoma uterine. Monga ulamuliro, sikukuvulaza Ndisanaumbidwe ndipo alibe angabweretse mavuto pobereka. Koma nthawi zina, akhoza kukumana ndi mavuto aakulu kwambiri.
Amniotic constriction - CHIKWANGWANI filaments, amene angabuke chikhodzodzo yoopsa. Iwo akhoza compress kapena kumangirira chingwe umbilical Ufumuyo kwa ziwalo za thupi la mwana wosabadwayo, kuchititsa vuto lobadwa (amputation wa manja, mapazi, zala, kapena phalanges, nthawi zina podulidwa ziwalo pang'opang'ono).
zifukwa
Pali ziphunzitso ziwiri chifukwa pali amniotic constriction. Chifukwa zodabwitsazi limafotokoza mobwerezabwereza utaphulika amniotic kuwira mu mimba msanga. Monga chorion silinasinthe, kuopseza kusokoneza chitukuko Ndisanaumbidwe si anati, koma ulusi amene angapeze chifukwa yopuma, free-akuyandama madzimadzi amniotic. Iwo akhoza zolumukizidwa ndi thupi la chipatso. M'kupita kwa mimba mwana chikamakula, koma ulusi akanali yemweyo monga iwo anali, choncho palibe psinjika a minofu ischemia ndipo necrosis.
Patapita nthawi, chiphunzitso chachiwiri, monga woyamba sunawakhutitse okayikira amene anaona kuti amniotic constriction (zingwe m'mimba mwa mayi woyembekezera) azaonekera imodzi ndi malformations ena obadwa nawo monga mphanga mlomo kapena abadwe. madokotala amenewa amanena kuti pali magulu chifukwa matenda mtima kapena matenda a makope yoopsa.
Baibulo lina kwa zinthu intrauterine matenda, ndi zoopsa woyembekezera, nthenda maliseche (anawaonjezera kuwirikiza kawiri la chiberekero, nyanga ziwiri chiberekero , ndi zina zotero. D.), m'bale Cin (khomo lachiberekero kulephera), kutupa amnion ndi, endometritis, oligohydramnios. Koma palibe mfundo awa anatsimikizira momveka.
diagnostics
Nthawi zambiri, matenda ndi zasayansi amalephera kuzindikira amniotic constriction. Photos pa phunziro ultrasound uninformative, kuyambira ulusi awa woonda kwambiri. Mwanjira mungamvetse miyendo zikuluzikulu ndi kutupa m'madera a psinjika. Makamaka ambiri overdiagnosis wa kudwala izi. Choncho, ngati dokotala ndi achifwamba pamaso pa magulu amniotic, pakati walangizidwa Kujambula ndi 3D ultrasound.
Anthu oposa theka la matenda kaduka amniotic pa ultrasound mobwerezabwereza si kuonedwa chifukwa chotupa awo.
ziwerengero
Malinga ndi luso zida akalandire chithandizo pafupipafupi amene wapezeka amniotic constriction lingayambire pakukhala 1: 1200 ku 1:15 000 genera. Akukhulupirira kuti mimba mazana awiri ndi zikwi khumi zimachitika chifukwa cha zimenezi. peresenti makumi asanu ndi atatu a chingwe cha Simonara deform zala ndi manja, ndipo peresenti khumi - ndi psinjika za chingwe umbilical. Kuti mapangidwe mfundo mu chingwe umbilical zikubweretsa hypoxia ndi antenatal yoopsa imfa.
Mwamwayi, ambiri diagnoses "amniotic gulu constriction" sagwirizana ndi chingwe matenda kapena fibrous musati amavutitsa kwambiri kwa mwana wosabadwayo.
chibadwa
Mwina kuti kaduka amniotic kuoneka woyembekezera, ndi yaing'ono kwambiri. Izi si matenda otengera kwa makolo. Childs, kutengera mapangidwe kapena chromosomal masinthidwe zimachitika symmetrically, ndipo mu nkhani iyi, ulusi Ufumuyo mwachisawawa kwathunthu. Ngati mimba woyamba mwana Nkhosi Simonara anati, sizitanthauza kuti ana wotsatira adzavulazidwa. Komanso, sizitanthauza kuti makolo amene anavutika utero amniotic gulu constriction, mwana wabadwa ndi malformations.
zotsatira
Ngakhale amniotic kaduka - si chakupha kudwala, zotsatira za izo ndi zokhumudwitsa kwambiri. Chifukwa chakuti magulu akhoza entangle mbali yoopsa ya thupi, kukhala lymph stagnation. Zimenezi zimabweretsa edema ndi necrosis. Atabadwa chotero nthambi ayenera udulidwe, kapena kukhala udzaphwanya-syndrome: ndi poizoni kuti akhala akukuchitirani mu nthambi zamizidwa ndi kusakhala, kugwera mu makope zokhudza zonse ndi ziwalo adzayamba poizoni mwana. Izi zingachititse kuti imfa yake. Choncho ndikofunikira kuchotsa ziwalo, ngati kale mwachisawawa. Ndipo mwamsanga.
Komanso, vuto la kaduka amniotic mwina matendawa, miyendo ndi zala mu gawo proximal ya nthambi. Pafupipafupi mwa ana awa msoko zala kapena phalanges zala ndi zala. Nthawi zina, kuwonjezera pa kaduka mwana ali anaona ena manyazi disembriogeneza: abadwe ndi chapamwamba mlomo. Nthawi zina kwambiri pali zotsutsana kwambiri msana ndipo mutu nkhope, eventration ziwalo m'mimba, atresia wa chingwe umbilical.
Ngati constriction amakhudza nsupa kwambiri spaced khungu, ndiye pa mfundo iyi izo aumbike hemangioma. Chotupa atabadwa ayenera kuchotsedwa.
Asayansi ena kupeza zingwe kugwirizana Simonara ndi clubfoot. Ichi ndi chifukwa miyendo yoopsa ndi kuliika CHIKWANGWANI chingwe, kotero chiberekero akhoza compress phazi la mwana wosabadwayo. peresenti makumi awiri cha kudwala izi ndi awiri amaganiza. Vuto lina, amene ayenera kupereka azamba - kubadwa msanga. Izi Vuto - chodabwitsa kawirikawiri mu mimba zimene zimachitika ndi matenda kaduka amniotic.
chithandizo
Monga ulamuliro, mu utero ndi matenda sungathe anawachiritsa. Mu yochizira matenda, pali milandu anecdotal kumene transvaginal kapena laparoscopic opaleshoni. Koma iyo inali muyeso kwambiri, monga ziwalo wotsinidwa kwambiri. Koma sikawirikawiri kwambiri amniotic constriction. Chithandizo nthawi zonse umachitikira pamene mwana wabadwa.
ulusi ndi kuligaŵa ndi udulidwe mbali ya chiwalo ngati n'koyenera. Kusintha khalidwe la moyo kuziika zala zida zake pansi.
kaonedwe
Kuti madokotala ananena zawo chifukwa ndi moyo, ndi zambiri yabwino. Ana nthawi zambiri kukula ndi kukhala mogwirizana ndi msinkhu. Chaka chilichonse miyendo bwino, kotero imfa ya mkono, dzanja m'munsi mwendo kapena phazi n'zotheka kufunsa wogwirizira yokumba. Ana amalimbikitsidwa kuti kusintha kupeza mano otere akamakula. Ngati constriction anachititsa zazing'ono zinchito chilema, zodzikongoletsera chilema angathe kuthetsedwa ndi zala kutengerapo ndi phalanges awo.
Mu anthu matendawa kaduka amniotic abadwe ana mwangwiro wathanzi, monga matenda si tinatengera.
Otchuka amene anali magulu Simonara
Izo zakhala nthawi imene anthu ndi nthambi amputation anabisalamo m'nyumba zawo ndipo ankadana ndi anthu. Tsopano iwo akhoza kukhala ndi pafupifupi palibe ufulu kugwira udindo wofunika anthu thupi, kuonekera pa TV ndiponso nawo mipikisano kukongola.
Anthu ena otchuka manyazi a kubadwa ndi amputation kobadwa nako, koma kaya chifukwa amniotic constriction - funso lofuna.
- Carrie Bornell - Ammayi, amene anabadwa opanda mkono bwino. Iwo amagwira ntchito pa televizioni ana a njira. Kwachititsa mchitidwe wosanganiza mwa amaonetsa wamng'ono ndipo makolo awo anali ngati kutsogolera kwa zikamera wa mndandanda wa mapulogalamu za mmene kuuza ana za olumala ndi mbali yapadera ya moyo wa anthu awa.
- Dzhim Ebbot ndi bwino kuti mafani onse a mpira. Iye ndi mtsuko lodziwika bwino, mwachitsanzo chakudya, popanda burashi bwino. Iye anapuma pa masewera kumapeto kwa zaka mazana makumi awiri, koma chitsanzo chake akupitiriza kuuzira anthu ambiri olumala ndiponso Paralympians.
- Teresa yukata - okongola Abiti America, anabadwa popanda dzanja lamanzere. Pa mpikisano, sindinkafuna kuvala prosthesis, kusonyeza kuti n'zotheka kukhala wokongola, ndipo palibe mbali yokumba.
- Lake Kelli Noks - pamwamba chitsanzo opanda mkono wakumanzere. Mu 2008, anapata zenizeni zimasonyeza pa BBC njira 3. Kuwonjezera pa mpikisano uwu nawo atsikana asanu ndi olumala zosiyanasiyana.
- Nikolas Makkarti - wotchuka limba, amene anabadwa popanda dzanja lamanja.
- Nikolas Vuychich - mlaliki Australia Mkhristu. Umatchuka ndi kubadwanso popanda miyendo iliyonse. Iye limafalitsa mabuku yake ndipo akupita kuti misonkhano padziko lonse monga chitsanzo, kuti simuyenera kusiya ngakhale mu zinthu zovuta kwambiri.
- Mark Goffeni - woyimba gitala, anabadwa ndi manja yonse. Iye anaphunzira kusewera ndi zala.
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