Thanzi, Matenda ndi zokwaniritsa
The etiology wa sarcoidosis ndi matenda ali kusokonezedwa ndi matenda Lefgrena
Lefgrena matenda - ndi symmetrical hilar mfundo bronchopulmonary lymphatic dongosolo mbali zonse. Disease limodzi ndi mawonetseredwe khungu (erythema nodosum), malungo, ndi arthralgia. zizindikiro ndi khalidwe la sarcoidosis.
Pamene matendawa amakhudza ziwalo zosiyana - mapapo, ndulu, lymph mfundo. Lefgrena syndrome sarcoidosis si opatsirana ndipo si matenda opatsirana. Osati kusokonezedwa ndi njira oncologic matenda ndi chifuwa chachikulu.
chithunzi matenda
Sarcoidosis wakhala ndithu nthawi yayitali matenda osowa, koma lero zinthu zasintha kudwala kufalikira pa kugunda kwambiri padziko lonse. Malinga ndi kafukufuku, kuposa wina aliyense kuvutika syndrome Lefgrena akazi kuyambira azaka 20 mpaka 40, koma matendawa akhoza kudza kwa munthu aliyense.
Zimakhala saonetsa zizindikiro, pang'onopang'ono kapena maonekedwe pachimake. chipatala Asymptomatic zambiri wapezeka ndi mwayi pa njira fluorography bwino. Ambiri ndi kupitirira mwapang'onopang'ono matenda ndi zizindikiro zotsatirazi:
- dyspnea pa yaikulu;
- mukupweteka ogontha chifuwa;
- ululu pakati pa masamba phewa ;
- youma chifuwa;
- otsika kalasi malungo ;
- kutopa ndi kufooka;
- kwambiri thukuta;
- kusafuna kudya;
- molumikizana mafupa kumbuyo m'munsi.
Pachimake kwa sarcoidosis amatchedwa matenda Lefgrena, izo limodzi ndi kuukitsa kutentha kwa 38-39 ° C, molumikizana mafupa, zotupa mu mawonekedwe a erythema, kupweteka m'chifuwa ndi kupuma movutikira. Si zachilendo ku pachimake pa kuchira bwino popanda kugwiritsa ntchito mankhwala anthu zachipatala zikunena ena.
The etiology matendawa
Mpaka mapeto a mankhwala odziwika zimayambitsa matenda, zikuoneka kuti tifulumizane izo ndi zinthu zotsatirazi angathe:
- matenda, Mycobacterium TB, matenda a chiwindi C;
- chowawa kunja zinthu, wina akapuma zitsulo fumbi;
- kusuta, amene si muzu, koma kwambiri complicates njira ya matenda;
- chibadwa.
Kupewa sarcoidosis
Odwala matenda Lefgrena tifunika kusiya kusuta, mofulumira kuchira. nthawi tifunika kufufuza ziwalo chifuwa mu zaka 2. Mogwirizana chakuti etiology cha matenda samadziwika mpaka mapeto, mfundo ya kanthu njira kuphunzira. Akatswiri amalangiza kuti musayandikire zitsulo fumbi ndi foci matenda.
Lefgrena syndrome sarcoidosis wapezeka zotsatirazi extrapulmonary kutanthauzira ndondomeko - kugonjetsa subcutaneous minofu, khungu ndi zotumphukira lymph mfundo. Pali ponso khomo lachiberekero, subclavian, axillary ndi mfundo inguinal. Nthawi zina, bwanji lymph mfundo za pamimba.
Bone ndi dongosolo chapakati mantha amakhudzidwa kwambiri kamodzikamodzi, koma n'zovuta kuti matenda zimachitika. Sarcoidosis mtima kumachitika mu 20-30% milandu ndi asymptomatic. kumanzere kwa mtima ndi kuchepetsedwa M'BUKU, lamanja ventricle ukuwonjezeka.
Kupenda oyambirira ndi mankhwala anapatsidwa mwayi kudalira ziyende bwino. Mu mulandu wina, pali kusintha mu minofu ya m'mapapo, yomwe n'kukumana ndi olumala.
Lefgrena syndrome pachimake sarcoidosis chimake
Nthawi zambiri kusokonezedwa ndi sarcoidosis, TB chifukwa cha kufanana zizindikiro. Izi zimafunika bwinobwino, chifukwa zimayambitsa ndi mankhwala osiyana. Palibe sangathe chinkhoswe kudzipatsa mankhwala, makamaka kutenga mankhwala anafuna odwala TB, ndiye kuti akhoza kuchita imfa.
Lefgrena syndrome (a Chitsanzo chachikulu tingachipeze powerenga) - uyu ndi pamene chikhalidwe ambiri wodwala ndi zogwira ziyenera. Pali kusintha mu khungu. Zingaoneke:
- papules ndi mipukutuyi;
- Chilblains lupus;
- keloid zipsera;
- infiltrates;
- erythema nodosum;
- SKD ndi CKD sarcoid Beck;
- mfundo angapo wandiweyani mu minofu subcutaneous.
diagnostics
Kufufuza syndrome odwala Lefgrena ndi kuchita X-ray. Monga njira kuukonza ntchito yopangidwa tomography. Kuchititsa amuzolengedwa ndipo magazi.
Vuto la mankhwala ndi kupondereza ndondomeko yotupa. Njira yabwino kwambiri ndi ntchito corticosteroids kwa miyezi sikisi. Ngati zingamvekere ziwalo zofunika chofunika glucocorticosteroid timadzi mankhwala.
Mofulumira mwapang'onopang'ono Inde mankhwala ndi nthawi yochepa ya utsogoleli mtsempha wa mankhwala odana ndi yotupa. Pa nthawi imene mankhwala ndi mphamvu, unachitikira plasmapheresis (magazi ayeretsedwe). Pa ovuta matenda siteji m'mapapo amafuna kuziika ziwalo. Njira ya matenda ndi mankhwala zotsatira kwakukulukulu yabwino, koma si kofunika kuyamba ndondomeko.
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