The anomaly wa Arnold Chiari Mtundu 1 - ndichiyani? Zizindikiro, zotsatira, mankhwala

Si chinsinsi kuti pa mapangidwe Ndisanaumbidwe m'mimba mayi akhoza kudwala osiyanasiyana kuphatikizapo anomaly wa Arnold Chiari mtundu 1. Kodi matenda? Madokotala kuitana zodabwitsazi kukanidwa kuti akufotokozera mu mwana wosabadwayo chifukwa mismatch wa kukula kwa chigaza ndi ubongo, kuyikidwa mu izo. Tikuyankhula zokhudza malo kumene cerebellum. Chifukwa ndi olakwika kumtunda kwa tonsils msana olekanitsidwa ndi siudzalandilidwa ngathi lamulo zina.

zimayambitsa

Kodi anthu abwinobwino kulibe, ngati wapezeka anomaly Arnold Chiari mtundu 1? Amayembekezeka kukhala ndi moyo, kuti madokotala, amadalira zifukwa zingapo: mlingo ndi maonekedwe a matenda. Musanayambe kuika matenda yomaliza, kudziwa matenda zinachititsa kuti chitukuko cha yofanana ndi:

1. Kobadwa nako. More mu utero yoopsa chigaza mapindikidwe kumachitika: fossa lili cerebellum, ndi chochepa kwa kukula ndi kupanga kanthu imvi. Mwa zifukwa zina kobadwa nako ukutchulidwa amphamvu kuwonjezeka foramen wa mwana wosabadwayo pa mapangidwe mafupa a.
2. Nagula. Woyamba ndi mutu choipa nthawi yobereka. Komanso mu gulu ili ndi msana choipa: kungasokoneze mowa wake - madzi wapadera, pakutchulidwa wa hydrocephalus ndi ena kuvutika msana.

Kukhala mosapita m'mbali, yeniyeni zifukwa asayansi sangathe koma itanani. Chinthu chokha chimene iwo tatsimikiza kuti matenda si kugwirizana ndi kuvutika chromosomal.

Zina mwa zifukwa

Aliyense akudziwa kuti nthawi ya trimester mimba, ndi mwana wosabadwayo amapita tsamba pafupifupi onse ziwalo. Choncho, njira yolondola ya moyo wa mayi ndi wofunika kwambiri pa chitukuko yachibadwa mwanayo. Ngati mkazi sakhala kutsatila malamulo zazikulu mtsogolo zimenezi zimachititsa kwambiri matendawo. Koma syndrome Chiari, chiopsezo pakuwonekera kwake ndi chinawonjezeka ndi zinthu zotsatirazi:

• Oipa mayi: kusuta fodya, kumwa mowa ndi mankhwala osokoneza bongo.
• Kugwiritsa ntchito mankhwala amphamvu, kudzikonda mankhwala.
• matenda anasamutsa tizilombo, makamaka chikuku.

Pa njira kuwala kwambiri ndi matenda obadwa mwana asaone mpaka mapeto a moyo zizindikiro zapadera, makamaka ngati wodwala matenda anomaly Arnold Chiari mtundu 1. Kodi ana ambiri moyo, amene ndi wachitatu kapena gawo lachinayi la matenda? Madotolo Zoneneratu zokhumudwitsa. Mwatsoka, ngati nthawi zambiri, ana aang'ono tidalamula imfa. Ngakhale mwanayo amapezeka woyamba kapena mtundu lachiwiri la matenda, ayenera mankhwala: opaleshoni, dzuwa ndi 85%.

mitundu syndrome

Kaya ukulu wake, iwo onse olumikizidwa ndi malo otsika kwambiri a cerebellum lapansi. The mozama ndipo amygdala pansi mu ngalande msana, matenda owopsa ndipo sizimadziwika: naye oterewa ndi kuvutika ena. Kuchokera pa ichi ndi kupereka 4 mitundu kudwala:

1. The anomaly wa Arnold Chiari Mtundu 1 - kodi mtundu uwu matenda? Kawirikawiri sayambitsa mavuto ena aliwonse mu chitukuko cha mwana. kusintha kandalama ubongo zimachokeradi, tonsils ndi ili m'dera khomo lachiberekero.
2. mtundu wachiwiri syndrome. Cerebellum pang'ono ankatembenukira mu foramen magnum, nthawi yomweyo pali Ndisanaumbidwe zosiyanasiyana kuvutika msana, ubongo ndi msana.
3. matenda ndi mtundu wachitatu. Kapangidwe cha hindbrain ndi kwathunthu ankatembenukira kwa foramen magnum. chophukacho aumbike mwa zone izi.
4. matenda Arnold Chiari ndi yachinayi. Iwo amakhala ndi cerebellar hypoplasia - underdevelopment ake. Komabe, sikuti iye kusuntha ndi amaganizira hydrocephalus ndi cysts kobadwa nako wa zapambuyo cranial fossa.

Madokotala amanena kuti kukana 2, 3 ndi 4 mtundu Kawirikawiri matenda limodzi ndi olumala ena aakulu mu chitukuko cha mwana: heterotopia wa kotekisi oziziritsa, subcortical nyumba hypoplasia, kuvutika kwa corpus callosum , ndi zina zotero.

Zizindikiro zazikulu

Monga tanenera kale, ngati siteji ya matenda ndi kuwala kwambiri, ndi ubongo mnzathuyu pang'ono, matenda angayambe pafupifupi moyo wake wonse, popanda kusokoneza munthu. Koma ili ndi vuto osowa. Kawirikawiri okhazikika ndi zonse mutu - ndi chizindikiro chachikulu cha matenda ndi anomaly wa Arnold Chiari mtundu 1. Zizindikiro za mtundu uwu wa migraine kupatula awa: kupweteka khosi, tinnitus, kunyansidwa ndi kusanza, kufooka kwa manja, tilinazo wa imfa ya nthambi, pamaso kutsogolo ndi masomphenya awiri, chosadziwika gait, kulankhula slurred, ndipo movutikira.

Pankhani ya matenda a mtundu wachiwiri, lomwe ndi woopsa kwambiri ndipo zovuta zizindikiro zake khalidwe kuoneka posachedwa atangobadwa kapena ndili wamng'ono kwambiri (zambiri mu sukulu). Kawirikawiri wheezing ndi phokoso kupuma makanda, kulira ofooka, kupuma ndi kumeza. ana amenewa yomweyo nakhalanso ndi akuyesa kupulumutsa kudzera opaleshoni. Mu milandu, chinthu chachikulu - musaphonye nthawi imene angathe kupulumutsa moyo wa mwana.

zizindikiro zina

Iwo anati mu madigirii kwambiri za matendawa. magwero yaikulu ya ubongo m'mnyewa wamtima kapena msana nthawi zambiri zizindikiro za anomalies Arnold Chiari 1 mtundu si loopsa ngati subspecies ake ena. Iwo yodziwika osati awiri masomphenya, koma khungu wathunthu, imfa ya chikumbumtima, imfa ya kuyenda, kenaka utentha mamba m'makona, mavuto ndi pokodza, kufooka kwa thupi, imfa ya kumverera mu mbali yaikulu ya thupi (nthawi zina ndi theka lonse la thupi).

Development wa zotsatira zosiyana thanzi kungachititse anomaly wa Arnold Chiari mtundu 1. Amayembekezeka kukhala ndi moyo ndi njira mwake zimadalira matenda mwamsanga ndi zolondola. Njira yokhayo kudziwa ndi kudwala ndi Kujambula (kulingalira maginito kumveka) ubongo. Pamafunika boma la kulephera kuyenda wathunthu wodwalayo, ana yogwira ali euthanized ndi mankhwala apadera. Mothandizidwa ndi chipangizo lino komanso kufufuza msana, msana, khomo lachiberekero ndi thoracic mafupa. Kujambula angazindikire osati matenda, koma pathologies zonse zimene zigwirizana pamodzi ndi matendawa.

zosokonezeka

Development wa pathologies zosiyanasiyana imfayo anomaly Arnold Chiari mtundu 1. Zotsatira zake zikhoza kukhala zosiyana kwambiri: kuchokera arachnoiditis aakulu, kutsiriza ndi zotupa parenchymal wa axon lapansi. Makamaka kwambiri mavuto izi zimachitika ndi maziko a matenda magazi mu zimakhala mitsempha. matenda Neuropsychiatric, mu nkhani imeneyi pambuyo anayesedwa mu mawonekedwe a kuchedwa mu chitukuko cha paraplegia. Ngati anomaly ndi kukula pang'onopang'ono kwambiri, tidzapeza hydrocephalus - kudzikundikira kwambiri a madzimadzi mu dongosolo yamitsempha yamagazi ubongo.

Komanso, Arnold Chiari syndrome zingachititse psinjika cholimba wa chingwe msana kuti munthu litaferatu. Pansi amadza zake zoipa amayamba kupanga cysts ndi cavities mu msana: amalandira madzi kuti akuswa msana ntchito. Ndi zotheka mavuto ndi kupuma mpaka mabasi. Nthawi zina madokotala analemba odwala chibayo congestive - kumakhaladi chifukwa chakuti munthu wotaya amatha momasuka.

chithandizo ndiwofatsa

matendawa mankhwala ndi njira ziwiri. Madokotala anasankha ndiwofatsa kapena opaleshoni njira malingana ndi zizindikiro ndi zizindikiro akuwonetseredwa mu mtima, popereka moyo wa munthu, zosokonezeka ndi zotsatira za matendawa. Nthawi zina yekha ndi mankhwala akhoza kulimbana ndi matenda monga Arnold Chiari mtundu 1 anomaly. Kodi mtundu wa mankhwala? Choyamba, dokotala mosalekeza amakhala chiphasochi chizolowezi cha wodwala, akutsogolera gulu kuti kuthandizira panzeru kwa akatswiri osiyanasiyana, amene atakambirana yoyenera adzakhala njira yoyenera.

Ngati wodwala anadandaula ululu m'dera occipital mutu kapena khosi, iye Kwalamulidwa othetsa ululu ndi wothandizila odana ndi yotupa, komanso mankhwala othandiza kumasuka minofu. Imathandiza kwambiri ndi wapadera achire zolimbitsa thupi - zolimbitsa thupi ndi umalimbana kuchotsa kuwalemekeza miyendo, ndi normalization wa mgwirizano. Pakuti zolinga zimenezi, monga momwe yolimbikira kuntchito mankhwala. Ndipo zambiri akhala akugwira magawo ndikuphunzitsidwa kulankhula, amene adzatha mavuto ndi kulankhula. Zonse mwa njira zimenezi akhoza akuchedwa kapena kwathunthu kuteteza pokwaniritsa chithandizo amtopola - opaleshoni.

alowererepo opaleshoni

Zimachitika kuti miyeso pamwamba sititenga - mwachangu akupitiriza kukhala ndi kupulumutsa gulu la ndikawapempha Arnold Chiari mtundu 1 anomaly. Chithandizo kusintha kwambiri: dokotala akuyamba kukonzekera munthu kwa opaleshoni. ntchito Neurosurgical wochititsidwa ndi mipherezero atatu. Choyamba, kuthetsa zizindikiro akuluakulu a matenda, monga imfa ya chikumbumtima, zipolowe zithunzi, kufooka minofu. Chachiwiri, alowererepo kumathandiza kuchotsa limatiphunzitsa zizindikiro - kuthetsa psinjika ubongo. Chachitatu, ntchito chifukwa ntchito mu mlingo wa kayendedwe ka mowa.

Alowererepo suspends ndondomeko ya kusintha mu dongosolo la msana ndi nkhani imvi: chifukwa cha zizindikiro za kuchepa, wodwalayo amayamba kuona bwino. Childs, madokotala ku kumbuyo kwa kuchotsedwa cranial fossa fupa mpukutu: danga kumawonjezera ubongo, vuto imvi ikutha kuti osamukira ndi cholizira. Komanso amachepetsa intracranial kuthamanga. Komanso, madokotala zikukangalika pogwiritsa ntchito njira monga kumezetsanitsa ndi kutsekera kwa ngalande msana.

kupewa

Kuti mwanayo analibe mavuto pamwamba, mayi woyembekezera ayenera kulingalira za chikhalidwe chawo. Choyamba, ayenera kuonanso kuvutika zonse zotheka kuti angagwe mu mwana wosabadwayo: malformations la chubu ubongo, Down a Syndrome, Arnold Chiari mtundu 1 anomaly. Kodi matenda, chifukwa zidzachitika, ndipo zimene tingatani kumwedwa kuchepetsa kufala kwa izi ndi zina kuvutika, ayenera kudziwa chilichonse mayi woyembekezera. Woyenera ndi kudziwa Mayi woyembekezera zidzatheke kupewa zinthu zonse kungasokoneze pa mapangidwe Ndisanaumbidwe lapansi.

Kachiwiri, mkazi ayenera kudya mokwanira, kudya zosiyanasiyana chakudya wathanzi: nsomba, nyama, zipatso, masamba, dzinthu ndi mkaka. Iwo mosamalitsa sikuloledwa mowa. Komanso, mufunika kuleka kusuta, osanenapo mankhwala ndi mankhwala osokoneza bongo. mankhwala ena aliwonse, ngakhale mwanjira, mayi woyembekezera amatenga pokhapokha mankhwala dokotala. Chachitatu, mkaziyo ali kwambiri kuyenda, kupuma mpweya wabwino kusuntha kwambiri. Za misempha, maganizo ndi malingaliro oipa ndi kuiwala, kusangalala udindo wake ndi kupeza chimwemwe kwambiri ndi moyo wanu.