Thanzi, Matenda ndi zokwaniritsa
Myasthenia Gravis: zizindikiro, matenda, mankhwala
Masiku ano, pali ambiri matenda autoimmune. Munthu angathe kuchotsa ndi thandizo la mankhwala bwino mwapadera, pamene ena salabadira chithandizo, ndipo chinthu chokha chimene angathe mankhwala - kuteteza exacerbations.
Nkhaniyi itithandiza kulankhula za matenda monga myasthenia gravis: zizindikiro, matenda ndi mankhwala a matenda - mphindi onsewa adzayesa kukambirana mokwanira monga momwe tingathere. Komanso, kupeza ndani kwambiri atengeke matenda, pali njira kupewa mavuto amenewa alipo.
Kodi myasthenia gravis?
Myasthenia gravis ndi matenda autoimmune zimene zimachititsa mwapang'onopang'ono minofu kufooka. Izi zimachitika chifukwa cha zolakwa ku HIV neuromuscular. Nthawi zambiri, minofu akhudzidwa cha maso, m'kamwa ndi nkhope, osachepera - kuchita ntchito kupuma.
Monga Kafukufuku amasonyeza, myasthenia gravis zambiri zimakhudza akazi a zaka zapakati, ngakhale zisakuyenda anayamba kulembedwa mwa achinyamata.
gulu la matenda
Vuto matenda wachinsinsi ndi mtundu. Ndinali nazonso, ndi myasthenia gravis. Mawonekedwe a matenda amadalira zinthu zosiyanasiyana Choncho, ife timayang'ana pa mitundu ambiri.
Kutengera ndi gulu la m'badwo wa myasthenia mtima gravis kungakhale:
- kobadwa nako;
- akhanda;
- mwana;
- akulu;
- Patapita Baibulo.
Malinga ndi zizindikiro matenda a matenda a mitundu otchedwa myasthenia gravis zotsatirazi:
- diso mawonekedwe;
- minofu ndi mafupa;
- pharyngeal-nkhope;
- zowombetsa mkota.
Zizindikiro za aliyense wa matenda inalongosola pansipa.
Zimayambitsa matenda
Chimayambitsa matenda Zatsala unexplored. Amadziwika yekha kuti matenda kumachitika chifukwa blockage wa dongosolo maselo mthupi mu minofu. Chifukwa, iwo sangathe kuyankha chifukwa chizindikiro ubongo.
The matenda myasthenia gravis kungakhale kobadwa nako kapena kugula. Mawonekedwe woyamba ndi n'kukhala kwambiri ndiponso zinthu zake masinthidwe chibadwa.
Kuthi myasthenia gravis angasonyeze pa maziko thymomegaly (otchedwa benign prostatic hyperplasia, thymus) kapena zotupa. Pasanathe ambiri, chifukwa cha matenda zingakhale ndi matenda autoimmune, monga matendawa kapena dermatomyositis.
Pali nthawi zambiri pamene myasthenia gravis anayamba ndi maziko a khansa. Kwenikweni, nkhawa chotupa ziwalo zoberekera (prostate, n'kuwasanganiza), osachepera - chiwindi, m'mapapo, ndi zina zotero.
zizindikiro
Kodi zizindikiro chingatithandize matenda, "myasthenia gravis"? Zizindikiro angakhale osiyana kapena amaphatikiza malingana mawonekedwe ndi gawo la matenda.
Ocular myasthenia gravis amakhudza:
- zozungulira minofu diso;
- minofu diso ;
- minofu, amene ali ndi udindo kutukula chikope chapamwamba.
Chifukwa, zizindikiro za mawonekedwe matenda mwina motere:
- vuto moganizira maso;
- strabismus;
- awiri masomphenya;
- ndikosatheka kwa nthawi yaitali kuyang'ana pa zinthu lakutali kapena kwambiri pafupifupi;
- kuŵeramitsa wa chikope chapamwamba (ptosis).
Last zizindikiro wa nkhani angasonyeze yekha madzulo ndi m'mawa kwina kwathunthu.
mawonekedwe kutsogolo kwa myasthenia gravis limodzi ndi zizindikiro:
- kusintha mawu, amene akukhala "mphuno" ndi akhungu;
- bvuto ndi mawu (wodwala amatopa ngakhale patapita mphindi yochepa basi kucheza);
- mavuto ndi kudya chakudya (wodwala zovuta kutafuna chakudya chotafuna chifukwa cha kufooka kwa minofu chogwirizana).
Ndi kugonjetsedwa kwa pharynx pali Mwina mkulu wa ingress madzi mu kapepala kupuma. Ichi ndi chifukwa chakuti wodwalayo sangathe kutenga chakudya chotafuna ndi zingalepheretse, zomwe zimachitika nthawi zambiri. Chifukwa, ndi zinadzala ndi chitukuko cha chibayo chiyembekezo.
mawonekedwe a minofu ndi mafupa a matenda limodzi ndi zowawa za gawo makamaka za thupi. Nthawi zambiri, imeneyi imagwira ntchito kwa nthambi. Pali milandu pamene wodwala ngakhale kumwa chikho mwachizolowezi a madzi kapena kukwera masitepe.
The owopsa ndi mtundu zowombetsa mkota wa matenda. Kumaonetsa kufooka kwa minofu kupuma, tingayambe hypoxia pachimake ndi imfa.
Monga mukuonera, myasthenia gravis, zizindikiro zimene ziri osiyanasiyana ndithu, ndi matenda aakulu kwambiri ndi moyo pachiswe. N'chifukwa chake n'kofunika kuona zikamera vuto ndi kukhwimitsa zonse zofunikira.
Choncho, zinthu zotsatirazi kuti ayankhidwa mu chimango cha mutu wakuti "Myasthenia Gravis" - matenda ndi mankhwala a matenda.
mathandizidwe ndi
Myasthenia Gravis - ichi ndithu matenda osowa. Choncho, katswiriyu sangathe nthawi zonse mofulumira kupanga matenda zolondola.
Kodi muyenera kuchita chiyani kudziwa matenda mankhwala monga myasthenia gravis? Matendawa ingakhale monga iyi:
- kafukufuku wa mtima pamaso pa madandaulo;
- matenda Kupenda;
- prozerinovoy kuchititsa mayesero;
- Mayeso ndi edrophonium;
- electromyographic phunziro;
- kudziwa mlingo wa chitetezo kwa maselo acetylcholine ku seramu wa;
- diso mayeso;
- yopangidwa tomography a chifuwa;
- Kujambula;
- onani ntchito m'mapapo.
Phunzirolo lili mkati, nkofunika kuthetsa matenda n'kotheka, zizindikiro zimene kumlingo wofanana ndi zizindikiro za myasthenia gravis. Mwachitsanzo, zingakhale bulbar matenda, matenda yotupa (kakhosi, encephalitis), chotupa lomenyera tsinde ubongo (hemangioblastoma, glioma), neuro-akulu matenda (myopathy, Guillain syndrome, ALS, etc.), matenda cerebrovascular (ischemic instult ) ndi zina zotero.
Mankhwala chithandizo cha myasthenia gravis
Malinga zizindikiro, ndi siteji ya matenda zosiyanasiyana mtundu Napempha kwa mankhwala.
Njira yoyamba amafuna mankhwala kuti kusintha mopupuluma kufala pa mphambano neuromuscular. Nthawi zambiri ntchito Mwaichi wothandizila ngati pharmacological monga "oksazil", "Neostigmine" "Pyridostigmine" ndi zina zotero. iwo onse ndi mtundu wofanana wa kanthu ndi kuonjezera ndende ya acetylcholine. Mankhwalawa ndi imathandiza ndiyotani pakuchotsa matenda mu magawo oyambirira a chitukuko, komanso pa isanayambike mavuto.
Chinthu chotsatira muyenera kuchita - ufulu kusintha madzi ndi electrolyte bwino mu thupi. Izi zimafunika kudya mokwanira ali B mavitamini ndi potaziyamu kuonetsetsa kagayidwe yachibadwa.
Kukula kwa matendawa amatenda kukhazikitsidwa kwa njira amtopola chithandizo. Iwo MUKACHULUKIDWE phwando mahomoni immunosuppressive. Ngakhale kuti mankhwala awa ali bwino analekerera ndi thupi, phindu la ntchito yawo ndi zotsatira kwambiri angathe mbali, makamaka pankhani kukhalabe osati thanzi, komanso moyo.
Samalani!
Pali mankhwala ena amene kutiletsa kuti matenda "myasthenia gravis". Zikuphatikizapo beta-blockers, salt magnesium, kashiamu muzikangana, mankhwala aminoglycosides, mahomoni a chithokomiro, asamakhale ndi nkhawa, morphine, opangidwa kuchokera kwinini, antipsychotics, barbiturates, ndi hypnotics kwambiri ndi mankhwala.
Komanso, tiyenera kukumbukira kuti aliyense mankhwala mankhwala akhoza kumwedwa pokhapokha yokumana ndi dokotala, kutenga nkhani makhalidwe onse akuyenda wa chamoyo.
Chithandizo ndi opaleshoni
mankhwala sikuti kubweretsa zotsatira anakhumba, ndi kuchotsa vuto. Choncho, nthawi zambiri zofunika kuti alowererepo pa opaleshoni. Izo, nawonso, zikuphatikizapo atagwirana kapena njira zingapo:
- mawotchi mpweya wabwino ngati n'zosatheka kupuma mowiriza;
- plasmapheresis magazi purifier a chitetezo nthenda, momwe ndondomeko ayenera ikuchitika pafupipafupi fupipafupi;
- mankhwala kuntchito ndi physiotherapy - njira izi ziwiri muchisiye matenda, koma akhoza kuthandiza wodwalayo kupirira kusinthasintha mphamvu minofu.
Komanso, kungakhale kofunika kuti kuchotsa kwa England thymus kupyolera opaleshoni.
Mapulaniwo mankhwala selo
Mtundu uwu wa ndiyotani pakuchotsa vuto sanabadwe zinatchuka koma M'pofunikanso kukumbukira ndi za iye.
Chithandizo ndi maselo tsinde zichokera kwa minofu adipose, zasonyeza mkulu Mwachangu okwanira mu nkhondo yolimbana ndi matenda. Amathandiza kuti kutambasuka pazipita nthawi ya chikhululukiro. maselo tsinde wathanzi kuthandiza kukonza njira ya kupuma ndi kumeza. Komanso, amathandiza kuti kuwonongedwa kwa ptosis mu nthawi yaifupi zotheka.
The njira ya mankhwala ndi pafupipafupi ka maselo tsinde mu thupi yekha perekani odziwa katswiri!
Mapa tsogolo
Ngakhale m'zaka za m'ma otsiriza, matenda a "Myasthenia" kuphedwa pafupi. Koma nthawi ikamapita, ndi mankhwala Kodi chilili. Pa nthawi, ife anayamba zosiyanasiyana wapadera kuti kupulumutsa miyoyo ndi kudzapeza nthawi ya chikhululukiro.
Pa nthawi yomweyo tiyenera kukumbukira kuti myasthenia gravis ndi matenda aakulu. Izi zikutanthauza kuti odwala ndi nthawi zonse kukhala pa mankhwala (kapena mitengo zonse) kuti mukhale ndi thanzi. N'kosavuta kwa ndikuganiza kuti khalidwe la moyo mu nkhani iyi mwina kwambiri zowawa.
Choncho ndikofunikira akunenanso kuti chabe matenda yake ya matenda chingaimitse kupitilira ake m'nthawi yake komanso kupewa mavuto.
muyambirenso kupewa
Tinakambirana za kudwala ichi monga myasthenia gravis. N'chiyani chimene limodzi ndi zizindikiro za matenda ndiponso ngati pali mankhwala a matenda, ikufotokozedwanso. Pomaliza Ndikufuna kukhala pa njira zopewera muyambirenso, monga odwala, nkhani imeneyi ndi zogwirizana kwambiri.
Choyamba, mawu ofunika pa nkhani kuti katswiriyu ndi. Pankhaniyi, Mulimonsemo sangakhoze kuphonya njira anakonza, koma mu chochitika zizindikiro lankhulani dokotala kumenyana, osati kudikira ulendo wotsatira.
Kachiwiri, m'pofunika kuonanso ngati n'koyenera, kusintha moyo wanu yachibadwa. Odwala myasthenia zinthu palibe payenera kukhala kutopa thupi, choncho m'pofunika kusankha ntchito, kupereka ntchito maganizo. Ngati n'kotheka, ayenera kuchepetsa nthawi ya ulendo, makamaka mabasi ndi magalimoto.
Tisaiwale kuti matenda alionse, ngakhale SARS, amachititsa nkhawa thupi ndi kusokonezeka kwa chitetezo cha m'thupi. Choncho n'kofunika kuti aziona kwambiri ukupeza awo, kuteteza hypothermia osati kukhala mu malo woipa lalikulu la anthu mu nthawi kuchuluka ambiri matenda opatsirana.
Pamaso pa myasthenia gravis kulandira mankhwala ena aliwonse ayenera anagwirizana ndi dokotala anu, chifukwa pali ambiri contraindications wapadera (ena anakumbukira kuyambira kumwamba).
Kodi musalankhule medicate ndi kukhala wathanzi!
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