Günther matenda - ndichiyani?

Pali akatswiri oona amene kwambiri kukhulupirira kuti nkhani zonse MIZUKWA ndi sayansi. Iwo akhoza kukhala mchikakamizo cha chotero matenda osowa monga matenda Günther kapena "cutaneous porphyria." matenda amaipitsa magazi kupanga chisokonezo mu kubalana a ngale ndi. Akukhulupirira kuti matenda Günther anali ambiri mu m'midzi ya Transylvania. Apo izo auka kwa aya yogwirizana.

Akatswiri amanena kuti kukanakhala kuti matenda, sitiyeneranso nkhani iliyonse ndi nthano za MIZUKWA Dracula ndi ngwazi zina ndi mano. Pafupifupi onse asymptomatic wodwala wayamba kwambiri matenda Günther a - lililonse mzukwa mafilimu.

Pezani vuto, ndi kufotokoza matenda adakwanisa m'nthawi ya 20. Zisanachitike izi anatengedwera pankhondo yaikulu ndi MIZUKWA kuti: kuchokera 1520 mpaka 1630 mu France yekha anaphedwa anthu oposa 30 sauzande, amene ankatengedwa MIZUKWA. Chozama mu dziko anadza kupyolera Chikhristu, koposa mwankhanza ankachitira anthu amene anagonjetsa mochedwa cutaneous porphyria.

Mawonekedwe zosowazi matenda majini zowawa ndi munthu mmodzi yekha pa 200 zikwi. Pankhaniyi, ngati vuto akuvutika kholo limodzi, kenako tikhoza kunena za 25% motsimikiza kuti matenda Günther zimaoneka ndi mwana.

Akukhulupirira kuti matenda - chifukwa cha pachibale. Medicine limafotokoza za 80 milandu porphyria pachimake pamene kunali kosatheka kuchiza. matenda Günther a amakhala ndi chakuti thupi si kubala Gawo magazi - maselo magazi wofiira. Ndipo izi zimaonekera mu kusowa kwa ayironi ndi mpweya magazi.

Mu zimakhala ndi magazi ndi kuphwanya kagayidwe pigment ndi chifukwa cha dzuwa liyamba apasuke hemoglobin. Komanso, ndondomeko izi zimachitika tendon mavuto amene zimabweretsa kupiringiza zala zina.

matenda Günther a amakhala ndi chakuti chuma (sanali mapuloteni mbali ya hemoglobin) adziwonetsa chinthu poizoni, amene angathe kuwononga minofu subcutaneous. Chifukwa cha zimenezi, khungu amakhala bulauni mu mtundu, thins ndi chiswa pambuyo anachita dzuwa. Pachifukwa ichi, pa nthawi khungu ndi zophimbidwa ndi zilonda ndi zipsera. Komanso, kutupa kuwononga makutu ndi mphuno, kwambiri deforming iwo.

Taganizirani za munthu ndi zala litapotanitsidwa ndi nkhope yokutidwa ndi zilonda ... Kwenikweni wowopsa? odwala amenewa chabe contraindicated dzuwa, chifukwa zimawabweretsera mavuto aakulu. Chikopa, yomwe ili pafupi ndi m'kamwa ndi milomo omangika ndi youma. Chifukwa cha pansi izi usinini pamtunda incisors, kupanga zoopsa mzukwa akumwetulira.

chizindikiro china cha matenda: mano kulephereka porphyrin, pachifukwa ichi, iwo akhoza kugula mtundu ofiira kapena pabuka-bulauni. Wodwala kwambiri wotumbululuka khungu chivundikirocho. Masana amadziona wamphamvu ulesi ndi kusowa mphamvu, mphamvu anabwerera yekha usiku. Dziwani amene anakhala lonse zizindikiro khalidwe chabe la matenda mochedwa siteji. Pali ena, kuli zoopsa mawonekedwe porphyria.

Mpaka theka lachiwiri la zana la 20, matenda Günther ankaona pafupifupi osachiritsika. Pali umboni wosonyeza kuti Zapakati, kuti magawowa alili iye anapatsidwa magazi atsopano kubwezeretsanso kupanda maselo magazi. Mwachibadwa, zimenezi sanapereke zotsatira, chifukwa boma bwino magazi, monga kumwa gawo lake, sikutheka.

Odwala porphyria sangathe kudya adyo, chifukwa asidi, amene anamasulidwa masamba iyi, ukuwonjezeka chifukwa kuwonongeka matenda. Disease porphyria zingachititse chongopeka, ntchito ziphe ena ndi mankhwala.