ThanziMatenda ndi zokwaniritsa

Hemolytic-uremic syndrome - ndichiyani?

Hemolytic uremic syndrome ndi chizindikiro, amene anawonetseredwa mu mawonekedwe a hemolytic magazi m'thupi, OPN ndi thrombocytopenia. Kwa nthawi yoyamba matendawa limafotokonzera 1955. Malinga ndi akatswiri, 70% milandu matenda ana a chaka choyamba cha moyo, ndi chabe zochitika zochepa zimene akuluakulu. M'nkhani ino tikambirana za matenda, komanso kuona mmene kuchitiridwa ndi njira yamakono ya hemolytic syndrome uremic.

zimayambitsa Zichitike

Chitukuko cha ichi akatswiri matenda pa tsiku lino amagwirizana ndi zifukwa zingapo. Kwenikweni izi tizilombo mwachindunji poizoni kuwonongeka capillary endothelium wotchedwa glomeruli. Pa chifukwa china dzanja angagone mu DIC ndiponso kuwonongeka mawotchi erythrocytes. Akukhulupirira kuti yotsirizira zikhoza kuonongeka pa kudutsa capillaries wa glomeruli okha, amene nawonso anadzazidwa ndi kuundana Ulimbo.

zizindikiro zazikulu

Hemolytic-uremic syndrome limapezeka ambiri mwa ana ndi kuchepa mofulumira linanena bungwe mkodzo, koma pakalibe zizindikiro zoonekeratu madzi m'thupi ndipo pa maziko a magawo ndi wabwinobwino VEO. Ngati mwana watentha thupi kapena kusanza anaonekera zambiri matenda amakula mwamsanga - panali edema ubongo. Nthawi zambiri, hemolytic syndrome uremic ndi lowonjezera ndi wotumbululuka khungu mwana, mu nthawi zina, ndi kuphulika yaing'ono.

Kupeza Vuto

Kuti kwaniritsa matenda monga matenda hemolytic-uremic, muyenera pochitika mndandanda wa mayesero, kuphatikizapo kusanthula wathunthu magazi. Only ndikatha kumfunsafunsa wonse wodwala kulankhula za chithandizo zina.

njira zamakono za chithandizo

More posachedwapa anapatsidwa matenda imfa anali amphamvu kwambiri (80 mpaka 100%). Komabe, asayansi zonse kufunafuna njira yothetsera vutoli. Choncho iwo unalengedwa zipangizo amatchedwa "yokumba impso" chifukwa chimene zinthu zasintha kopambana. Lero, imfa pafupifupi sizidzachitikanso (awiri ndi khumi peresenti). Iwo akhoza kukhala basi pa kudziwika matenda mochedwa, komanso chitukuko cha njira sizingasinthe mu ubongo chifukwa kutupa ake. Tikumbukenso kuti matenda ndi atypical hemolytic uremic syndrome, ambiri amafuna kuchokera magawo 2 9 (tsiku) ntchito "impso yokumba". Ndi dialysis izi akatswiri akhoza akhalebe amphamvu wabwinobwino wa metabolites, komanso kuteteza ubongo kutupa.

kaonedwe

njira zamakono kulola ana kulimbana ndi vutoli. Komabe, izi ndi zotheka kukachitika kuti matenda anali atazindikira mwa magawo ake oyambirira. Apo ayi, mosavuta mokwanira achire penapake m'munsi. Akatswiri amanena zinthu pakalibe kuyankha zabwino pa mbali ya thupi pambuyo magawo 2-3 ya hemodialysis, maulosi akumane kwambiri.

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